Monophasic Synovial Sarcoma of Pharynx: A Diagnostic Challenge

Gurshinder Pal Singh, Sandeep Dachuri, Shaila T Bhat, Ankur Kaur Shergill

Abstract


Synovial Sarcomas of the head and neck region are very rare. The histologic monophasic variant of this tumor in the pharynx is even more uncommon. The benign appearance of an otherwise aggressive neoplasm offers a diagnostic challenge to both the surgeons and pathologists worldwide. Immunohistochemistry augments the conventional histopathology and offers a definitive diagnosis. Surgery forms the main mode of treatment followed by adjuvant radiotherapy. A rare case of monophasic synovial sarcoma of pharynx of a young boy is reported here. Any benign appearing chronic lesion with sudden exacerbation in head and neck region in young age group should be envisaged with high index of suspicion.


Keywords


Diagnosis; Immunohistochemistry; Pharynx; Sarcoma; Synovial; Radiotherapy.

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References


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