Calcifying Cystic Odontogenic Tumor Presenting as a Dentigerous Cyst: A Case Report with Literature Review

Ali Hanttash AbuHanttash, Aysegul Tuzuner Oncul, Umit Akal Aktaş


The calcifying cystic odontogenic tumor is comparatively rare in occurrence, constituting about 1.6% - 4.3% of all odontogenic tumors. Various terminologies have been used to describe this rare odontogenic tumor, sometimes referred to as the “keratinizing and calcifying odontogenic cyst, Gorlin cyst, calcifying odontogenic cyst, calcifying ghost cell odontogenic tumor, dentinogenic ghost cell tumor, and epithelial odontogenic ghost cell tumor”. It is characterized by the presence of ghost cells with proliferative odontogenic epithelium and has a propensity for calcification. The aim of this paper is to report a case of calcifying cystic odontogenic tumor misdiagnosed as a dentigerous cyst in the posterior region of the mandible associated with unerupted tooth, along with a brief review of literature based on the term calcifying cystic odontogenic tumor. The lesion was surgically enucleated. After enucleation no recurrence has been observed during the follow up period of four years.


Calcifying Cystic Odontogenic Tumour; Dentigerous Cyst; Ghost Cells; Hybrid Odontogenic Tumor; Odontogenic Tumors

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